Vestnik dermatologii i venerologiiVestnik dermatologii i venerologiiВестник дерматологии и венерологии0042-46092313-6294Rossijskoe Obschestvo Dermatovenerologov i Kosmetologov29210.25208/0042-4609-2017-93-1-12-20ORGANIZATION OF HEALTH CARE AND EPIDEMIOLOGYЭПИДЕМИОЛОГИЯClinical features of mastocytosis at pediatric patientsКлинические особенности мастоцитоза у пациентов детского возрастаProshutinskayaD. V.ПрошутинскаяД. В.
Russian Federation
diana.dika@mail.ruMakoveckayaO. S.МаковецкаяО. С.
Russian Federation
State Research Center of Dermatovenereologyand Cosmetology, Ministry of Healthcare of the Russian FederationФГБУ «Государственный научный центр дерматовенерологии и косметологии» Минздрава России24022017931122024082017Copyright ©; 2017, Proshutinskaya D.V., Makoveckaya O.S.Copyright ©; 2017, Прошутинская Д.В., Маковецкая О.С.2017Proshutinskaya D.V., Makoveckaya O.S.Прошутинская Д.В., Маковецкая О.С.https://creativecommons.org/licenses/by/4.0https://vestnikdv.ru/jour/article/view/292

Mastocytosis is relevant to heterogeneous disease group characterized with redundant accumulation and proliferation of mast cells in tissues. The skin form of mastocytosis is mainly occurs in children. The article contains the current data on etiology, pathogenesis, classification, clinical forms, diagnosis, prophylactics and mastocytosis treatment at children.

Мастоцитоз относится к гетерогенной группе заболеваний, обусловленных чрезмерным накоплением и пролиферацией в тканях тучных клеток. У детей встречается преимущественно кожная форма мастоцитоза. В статье приведены современные данные об этиологии, патогенезе, классификации, клинических формах, диагностике, профилактике и лечении мастоцитоза у детей.

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