Vestnik dermatologii i venerologiiVestnik dermatologii i venerologiiВестник дерматологии и венерологии0042-46092313-6294Rossijskoe Obschestvo Dermatovenerologov i Kosmetologov51910.25208/0042-4609-2019-95-5-7-16REVIEWSОБЗОР ЛИТЕРАТУРЫModern diagnostic methods of paraneoplastic pemphigusСовременные методы диагностики паранеопластической пузырчаткиLepekhovaA. A.ЛепеховаА. А.
Russian Federation

Anfisa A. Lepekhova — Cand. Sci. (Med.), Assoc. Prof., V. A. Rakhmanov Department of Skin and Sexually Transmitted Diseases

Анфиса Александровна Лепехова — к.м.н., доцент кафедры кожных и венерических болезней им. В. А. Рахманова

anfisa.lepehova@yandex.ruTeplyukN. P.ТеплюкН. П.
Russian Federation

Natalia P. Teplyuk — Dr. Sci. (Med.), Prof., V. A. Rakhmanov Department of Skin and Sexually Transmitted Diseases

Наталия Павловна Теплюк — д.м.н., профессор кафедры кожных и венерических болезней им. В. А. Рахманова

teplyukn@gmail.comBolotovaI. M.БолотоваИ. М.
Russian Federation

Irina M. Bolotova — Student

Ирина Михайловна Болотова — студент

irinak120220@gmail.comI. M. Sechenov First Moscow State Medical University, Ministry of Health of the Russian FederationПервый Московский государственный медицинский университет им. И. М. Сеченова (Сеченовский университет)Pirogov Russian National Research Medical University, Ministry of Health of the Russian FederationРоссийский национальный исследовательский медицинский университет им. Н. И. Пирогова Министерства здравоохранения Российской Федерации171220199557161712201917122019Copyright ©; 2019, Lepekhova A.A., Teplyuk N.P., Bolotova I.M.Copyright ©; 2019, Лепехова А.А., Теплюк Н.П., Болотова И.М.2019Lepekhova A.A., Teplyuk N.P., Bolotova I.M.Лепехова А.А., Теплюк Н.П., Болотова И.М.https://creativecommons.org/licenses/by/4.0https://vestnikdv.ru/jour/article/view/519

Paraneoplastic pemphigus (PNP) is one of the least investigated and rare forms of bullous dermatoses, which comes from underlying neoplasm. The article presents a literature review of dermatologist`s longstanding international experience about etiology, pathogenesis, diagnostics and treatment of this disease. According to the research results of native and foreign authors systematization of modern diagnostic methods of PNP and detectable antigens was performed.

Conflict of interest: the authors state that there is no potential conflict of interest requiring disclosure in this article.

Паранеопластическая пузырчатка (ПНП) — одна из наименее изученных и редких форм буллезных дерматозов, протекающих на фоне неоплазии. В данной статье представлен литературный обзор многолетнего международного опыта дерматологов в отношении этиологии, патогенеза, диагностики и лечения данного заболевания. По результатам исследований отечественных и зарубежных авторов произведена систематизация современных методов диагностики ПНП и выявляемых при этом антигенов.

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