Progressive symmetric eritrocarotodermia Gottron: A rare case

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Abstract


The article deals with ethiopathogenetic factors of origin of progredient symmetric erythrokeratodermia of Gottron which is mainly characterized by autosomal dominant mode of inheritance and is classified as a disorder of cornification with extra epidermal cellular proliferation.

Clinicopathologic criteria on the basis of which this pathology can be verified are described here, such as: onset of a disease at an early age, strictly divided polycyclic, fixed, hyperkeratotic plaques with a narrow erythematic crown and a clean-cut, sometimes hyper pigmented edge, which are symmetrically located on skin on head, buttocks, limbs and are not prone to quick peripheral growth; large frequency of palmoplantar keratoderma and also histological changes typical of erythrokeratodermia.

The article describes a rare clinical case of autosomal-recessive progredient symmetric erythrokeratodermia of Gottron which is distinguished by seasonal changes of skin pathological process — emergence of rash in winter and complete remissions in summer.


About the authors

M. M. Tlish

Kuban State Medical Universit y, Ministry of Health of the Russian Federation

Email: fake@neicon.ru

Russian Federation

Marina M. Tlish — Dr. Sci. (Med.), Assoc. Prof., Head of the Department, Department of Dermatovenerology

tel.: +7 (918) 419-67-47

N. L. Sycheva

Kuban State Medical Universit y, Ministry of Health of the Russian Federation

Email: fake@neicon.ru

Russian Federation

Natalya L. Sycheva — Cand. Sci. (Med.), Research Assistant, Department of Dermatovenerology

tel.: +7 (918) 212-27-42

N. A. Boyko

City Clinic, LLC

Email: fake@neicon.ru

Russian Federation

Natalia A. Boyko — Cand. Sci. (Med.), Dermatovenerologist

tel.: +7 (918) 044-11-33

M. E. Shavilova

Kuban State Medical Universit y, Ministry of Health of the Russian Federation

Author for correspondence.
Email: marina@netzkom.ru

Russian Federation

Marina E. Shavilova* — Research Assistant, Department of Dermatovenerology

tel.: +7 (928) 467-88-93

F. A. Psavok

Kuban State Medical Universit y, Ministry of Health of the Russian Federation

Email: fake@neicon.ru

Russian Federation

Fatima A. Psavok — Cand. Sci. (Med.), Research Assistant, Department of Dermatovenerology

tel.: +7 (918) 960-33-57

References

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