Progressive symmetric eritrocarotodermia Gottron: A rare case

Cover Page


Cite item

Full Text

Abstract

The article deals with ethiopathogenetic factors of origin of progredient symmetric erythrokeratodermia of Gottron which is mainly characterized by autosomal dominant mode of inheritance and is classified as a disorder of cornification with extra epidermal cellular proliferation.

Clinicopathologic criteria on the basis of which this pathology can be verified are described here, such as: onset of a disease at an early age, strictly divided polycyclic, fixed, hyperkeratotic plaques with a narrow erythematic crown and a clean-cut, sometimes hyper pigmented edge, which are symmetrically located on skin on head, buttocks, limbs and are not prone to quick peripheral growth; large frequency of palmoplantar keratoderma and also histological changes typical of erythrokeratodermia.

The article describes a rare clinical case of autosomal-recessive progredient symmetric erythrokeratodermia of Gottron which is distinguished by seasonal changes of skin pathological process — emergence of rash in winter and complete remissions in summer.

About the authors

M. M. Tlish

Kuban State Medical Universit y, Ministry of Health of the Russian Federation

Email: fake@neicon.ru

Marina M. Tlish — Dr. Sci. (Med.), Assoc. Prof., Head of the Department, Department of Dermatovenerology

tel.: +7 (918) 419-67-47

Russian Federation

N. L. Sycheva

Kuban State Medical Universit y, Ministry of Health of the Russian Federation

Email: fake@neicon.ru

Natalya L. Sycheva — Cand. Sci. (Med.), Research Assistant, Department of Dermatovenerology

tel.: +7 (918) 212-27-42

Russian Federation

N. A. Boyko

City Clinic, LLC

Email: fake@neicon.ru

Natalia A. Boyko — Cand. Sci. (Med.), Dermatovenerologist

tel.: +7 (918) 044-11-33

Russian Federation

M. E. Shavilova

Kuban State Medical Universit y, Ministry of Health of the Russian Federation

Author for correspondence.
Email: marina@netzkom.ru

Marina E. Shavilova* — Research Assistant, Department of Dermatovenerology

tel.: +7 (928) 467-88-93

Russian Federation

F. A. Psavok

Kuban State Medical Universit y, Ministry of Health of the Russian Federation

Email: fake@neicon.ru

Fatima A. Psavok — Cand. Sci. (Med.), Research Assistant, Department of Dermatovenerology

tel.: +7 (918) 960-33-57

Russian Federation

References

  1. Скрипкин Ю. К., Бутов Ю. С. Клиническая дерматовенерология: руководство для врачей: в 2-х т. М.: ГЭОТАР-Медиа, 2009. [Skripkin Yu. K., Butov Yu. S. Clinical dermatovenereology: a guide for doctors: in 2 vol. Moscow: GEOTAR-Media, 2009. (In Russ.)]
  2. Naveen K. N., Pai V. V., Divyashree R. A., Athaniker S. B., Rao R. K. Progressive symmetric erythrokeratoderma with seasonal variation — an unusaual case report. Egyptian Dermatology Online Journal. 2012;8(2):10.
  3. Yan H. B., Zhang J., Liang W., Zhang H. Y., Liu J. Y. Progressive symmetric erythrokeratoderma: Report of a Chinese family. Indian J Dermatol Venereol Leprol. 2011;77(5):597–600.
  4. Калюжная Л. Д. Эритрокератодермия прогрессирующая симметричная. Клиническая иммунология. Аллергология. Инфектология. 2012;(1):73–78. [Kalyuzhnaya L. D. Erythrokeratoderma progressing symmetrically. Klinicheskaya immunologiya. Allergologiya. Infektologiya. 2012;(1):73–78. (In Russ.)]
  5. Van Steensel M. A., Oranje A. P., van der Schroeff J. G., Wagner A., van Geel M. The missense mutation G12D in connexin30.3 can cause both erythrokeratodermia variabilis of Mendes da Costa and progressive symmetric erythrokeratodermia of Gottron. Am J Med Genet A. 2009;(149):657–661.
  6. Прошутинская Д. В., Текучева Л. В., Трофимчук И. А., Катунина О. Р., Балабекова Ф. Г. Случай вариабельной эритрокератодермии Мендеса да Коста (Mendes da Costa) у ребенка 3 лет. Вестник дерматологии и венерологии. 2012;1:56–61. [Proshutinskaya D. V., Tekucheva L. V., Trofimchuk I. A., Katunina O. R., Balabekova F. G. A case of erythrokeratodermia variabilis (Mendes da Costa type) in a three-year-old child. Vestnik dermatologii i venerologii. 2012;(1):56–61. (In Russ.)]
  7. Guaraldi Bde M., Jaime T. J., Guaraldi Rde M., Melo D. F., Nogueira O. M., Rodrigues N. Progressive symmetrical erythrokeratodermia — Case report. An Bras Dermatol. 2013;88(1):109–112.
  8. Fatima F., Kapadia N., Farooqi M., Noshad M., Athar S., Faisal S. et al. A young girl with progressive symmetrical erythrokeratoderma and short height. Journal of Pakistan Association of Dermatologists. 2013;23(2):225–228.
  9. Цветкова Г. М., Мордовцева В. В., Вавилов А. М., Мордовцев В. Н. Патоморфология болезней кожи. М.: Медицина, 2003. [Tsvetkova G. M., Mordovtseva V. V., Vavilov A. M., Mordovtsev V. N. Pathomorphology of Skin Diseases. Moscow: Meditsina, 2003. (In Russ.)]
  10. Тлиш М. М. Клинико-статистическое подтверждение терапевтической прогрессивности авторских приемов немедикаментозной коррекции показателей биохимического и иммунологического статуса больных зудящими дерматозами. Кубанский научный медицинский вестник. 2013;1(136):166–171. [Tlish M. M. Clinical and statistical evidence of therapeutic progressivity Copyright adjusting for non-pharmacological methods of biochemical and immunological status of patients with pruritic dermatoses. Kubanskij nauchnyj medicinskij vestnik. 2013;1(136):166–171. (In Russ.)]
  11. Hirano S. A., Harvey V. M. From progressive symmetric erythrokeratoderma to erythrokeratoderma variabilis progressive. J Am Acad Dermatol. 2010;64(5):81–82.
  12. Тлиш М. М., Сычева Н. Л., Осмоловская П. С., Псавок Ф. А. Линейный эпидермальный веррукозный воспалительный невус (ilven). Вестник дерматологии и венерологии. 2017;3:53–57. [Tlish M. M., Sycheva N. L., Osmolovskaya P. S., Psavok F. A. Inflammatory linear verrucous epidermal naevus (ilven). Vestnik dermatologii i venerologii. 2017;(3):53–57. ( In Russ.)]

Supplementary files

Supplementary Files
Action
1. JATS XML
Download

Copyright (c) 2019 Tlish M.M., Sycheva N.L., Boyko N.A., Shavilova M.E., Psavok F.A.

Creative Commons License
This work is licensed under a Creative Commons Attribution 4.0 International License.
СМИ зарегистрировано Федеральной службой по надзору в сфере связи, информационных технологий и массовых коммуникаций (Роскомнадзор).
Регистрационный номер и дата принятия решения о регистрации СМИ: серия ПИ № ФС 77 - 60448 от 30.12.2014.


This website uses cookies

You consent to our cookies if you continue to use our website.

About Cookies