Aggressive systemic mastocytosis with skin involvement, the type of generaled urticaria pigmentosa (clinical case)

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Abstract


The authors describe the clinical observation of a case of the aggressive systemic mastocytosis with skin involvement, the type of generalized urticaria pigmentosa. They also present literature data concerning the etiology, pathogenesis, diagnosis and treatment of dermatosis.

About the authors

E. V. Sokolovskiy

First Pavlov State Medical University of St. Petersburg

Author for correspondence.
Email: noemail@neicon.ru

Russian Federation

V. V. Iastrebov

First Pavlov State Medical University of St. Petersburg

Email: noemail@neicon.ru

Russian Federation

A. V. Shcherbatykh

First Pavlov State Medical University of St. Petersburg

Email: alyona_shch@bk.ru

Russian Federation

E. R. Machulaitene

First Pavlov State Medical University of St. Petersburg

Email: noemail@neicon.ru

Russian Federation

References

  1. Skripkin Ju.K., Butova Ju.S., Ivanov O. L. Dermatology. National guideline. M: GJeOTAR-Media; 2013; 896. [Скрипкин Ю. к., Бутова Ю. С., Ив анов О. Л. Дерматовенерология. Национальное руководство. м: ГЭОТАР-Медиа; 2013; 896.]
  2. Rahmatullina N. M., Garifullina G. Z. Clinical cases of mastocytosis in medical practice; Kazanskij medicinskij zhurnal 2015; 96: (4): 598-601. [Рахматуллина Н. М., Гарифуллина Г. З. Клинические случаи мастоцитоза во врачебной практике. казан мед журн 2015; 96: (4): 598-601.]
  3. Belozjorova V. L., Bondarenko N. P., Bondarenko M.Ju. Case mastocytosis of newborn child; Medichni perspektivi; 2011; (2): 68- 72. [Белозерова В. Л., Бондаренко Н. П., Бондаренко М.Ю. Клинический случай мастоцитоза у новорожденного ребенка. Медични перспективи. 2011; (2): 68-72.]
  4. Maud A. W. Hermans, Mark J. A. Rietveld, Jan A. M. van Laar, Virgil A. S. H. Dalm, Maurice Verburg, Suzanne G. M. A. Pasmans, Roy Gerth van Wijk, P. Martin van Hagen, Paul L. A. van Daele. Systemic mastocytosis: A cohort study on clinical characteristics of 136 patients in a large tertiary centre. Eur J Inter Med 2016; (5): 25-30.
  5. Pal’cev M. A., Potekaev N. I., Kazanceva I. A., Krjazheva S. S. Clinico-morphological diagnostics and principles of treatment of skin diseases. Guidelines for doctors. M: Medicina 2010; 230-234. [Пальцев М. А., Потекаев Н. И., Казанцева И. А., Кряжева С. С. Клиникоморфологическая диагностика и принципы лечения кожных болезней. Руководство для врачей. М: Медицина 2010; 230-234.]
  6. Animesh Pardanani MBBS, PhD, Ayalew Tefferi MD; Systemic mastocytosis in adults: 2013 update on diagnosis, risk stratification, and managment. Am J Hematol 2013; (5): 612-624.

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